A2TJ54 CLN5_SHEEP Bis(monoacylglycero)phosphate synthase CLN5 [...] CLN5 , BMPSOvis aries (Sheep) 361 AA Q93100 KPBB_HUMAN Phosphorylase b kinase regulatory subunit beta [...] PHKB Homo sapiens (Human) 1,093 AA Q68CP4 HGNAT_HUMAN Heparan-alpha-glucosaminide N-acetyltransferase [...] HGSNAT , TMEM76Homo sapiens (Human) 663 AA Q04446 GLGB_HUMAN 1,4-alpha-glucan-branching enzyme [...] GBE1 Homo sapiens (Human) 702 AA P54802 ANAG_HUMAN Alpha-N-acetylglucosaminidase [...] NAGLU , UFHSD1Homo sapiens (Human) 743 AA P34949 MPI_HUMAN Mannose-6-phosphate isomerase [...] MPI , PMI1Homo sapiens (Human) 423 AA P51688 SPHM_HUMAN N-sulphoglucosamine sulphohydrolase [...] SGSH , HSSHomo sapiens (Human) 502 AA O14773 TPP1_HUMAN Tripeptidyl-peptidase 1 [...] TPP1 , CLN2, GIG1, UNQ267/PRO304Homo sapiens (Human) 563 AA P17050 NAGAB_HUMAN Alpha-N-acetylgalactosaminidase [...] NAGA Homo sapiens (Human) 411 AA P50897 PPT1_HUMAN Palmitoyl-protein thioesterase 1 [...] PPT1 , CLN1, PPTHomo sapiens (Human) 306 AA P15586 GNS_HUMAN N-acetylglucosamine-6-sulfatase [...] GNS Homo sapiens (Human) 552 AA P07602 SAP_HUMAN Prosaposin [...] PSAP , GLBA, SAP1Homo sapiens (Human) 524 AA P10253 LYAG_HUMAN Lysosomal alpha-glucosidase [...] GAA Homo sapiens (Human) 952 AA O15118 NPC1_HUMAN NPC intracellular cholesterol transporter 1 [...] NPC1 Homo sapiens (Human) 1,278 AA P06280 AGAL_HUMAN Alpha-galactosidase A [...] GLA Homo sapiens (Human) 429 AA P08559 ODPA_HUMAN Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial [...] PDHA1 , PHE1AHomo sapiens (Human) 390 AA P04062 GBA1_HUMAN Lysosomal acid glucosylceramidase [...] GBA1 , GBA, GC, GLUCHomo sapiens (Human) 536 AA