Q96RR1 PEO1_HUMAN Twinkle mtDNA helicase [...] TWNK , C10orf2, PEO1Homo sapiens (Human) 684 AA P54098 DPOG1_HUMAN DNA polymerase subunit gamma-1 [...] POLG , MDP1, POLG1, POLGAHomo sapiens (Human) 1,239 AA P12235 ADT1_HUMAN ADP/ATP translocase 1 [...] SLC25A4 , AAC1, ANT1Homo sapiens (Human) 298 AA O60783 RT14_HUMAN Small ribosomal subunit protein uS14m [...] MRPS14 Homo sapiens (Human) 128 AA Q5JTZ9 SYAM_HUMAN Alanine--tRNA ligase, mitochondrial [...] AARS2 , AARSL, KIAA1270Homo sapiens (Human) 985 AA Q6P2C8 MED27_HUMAN Mediator of RNA polymerase II transcription subunit 27 [...] MED27 , CRSP34, CRSP8Homo sapiens (Human) 311 AA Q9H9J2 RM44_HUMAN Large ribosomal subunit protein mL44 [...] MRPL44 Homo sapiens (Human) 332 AA O00142 KITM_HUMAN Thymidine kinase 2, mitochondrial [...] TK2 Homo sapiens (Human) 265 AA Q8N983 RM43_HUMAN Large ribosomal subunit protein mL43 [...] MRPL43 Homo sapiens (Human) 215 AA Q9BR39 JPH2_HUMAN Junctophilin-2 [...] JPH2 , JP2Homo sapiens (Human) 696 AA Q9Y276 BCS1_HUMAN Mitochondrial chaperone BCS1 [...] BCS1L , BCS1Homo sapiens (Human) 419 AA Q7LG56 RIR2B_HUMAN Ribonucleoside-diphosphate reductase subunit M2 B [...] RRM2B , P53R2Homo sapiens (Human) 351 AA P28289 TMOD1_HUMAN Tropomodulin-1 [...] TMOD1 , D9S57E, TMODHomo sapiens (Human) 359 AA O95363 SYFM_HUMAN Phenylalanine--tRNA ligase, mitochondrial [...] FARS2 , FARS1, HSPC320Homo sapiens (Human) 451 AA Q9HD40 SPCS_HUMAN O-phosphoseryl-tRNA(Sec) selenium transferase [...] SEPSECS , TRNP48Homo sapiens (Human) 501 AA Q9Y4W6 AFG32_HUMAN Mitochondrial inner membrane m-AAA protease component AFG3L2 [...] AFG3L2 Homo sapiens (Human) 797 AA O60313 OPA1_HUMAN Dynamin-like GTPase OPA1, mitochondrial [...] OPA1 , KIAA0567Homo sapiens (Human) 960 AA Q13501 SQSTM_HUMAN Sequestosome-1 [...] SQSTM1 , ORCA, OSILHomo sapiens (Human) 440 AA Q8CIW5 PEO1_MOUSE Twinkle mtDNA helicase [...] Twnk , Peo1Mus musculus (Mouse) 685 AA Q96A46 MFRN2_HUMAN Mitoferrin-2 [...] SLC25A28 , MFRN2, NPD016Homo sapiens (Human) 364 AA Q99N89 RM43_MOUSE Large ribosomal subunit protein mL43 [...] Mrpl43 Mus musculus (Mouse) 183 AA Q80WJ4 Q80WJ4_MOUSE Putative T7-like mitochodrial DNA helicase twinky variant Mus musculus (Mouse) 27 AA Q80WJ5 Q80WJ5_MOUSE Putative T7-like mitochodrial DNA helicase twinkle Mus musculus (Mouse) 76 AA