P42765 THIM_HUMAN 3-ketoacyl-CoA thiolase, mitochondrial [...] ACAA2 Homo sapiens (Human) 397 AA O75380 NDUS6_HUMAN NADH dehydrogenase [ubiquinone] iron-sulfur protein 6, mitochondrial [...] NDUFS6 Homo sapiens (Human) 124 AA P30084 ECHM_HUMAN Enoyl-CoA hydratase, mitochondrial [...] ECHS1 Homo sapiens (Human) 290 AA P03897 NU3M_HUMAN NADH-ubiquinone oxidoreductase chain 3 [...] MT-ND3 , MTND3, NADH3, ND3Homo sapiens (Human) 115 AA P50416 CPT1A_HUMAN Carnitine O-palmitoyltransferase 1, liver isoform [...] CPT1A , CPT1Homo sapiens (Human) 773 AA Q969Y2 GTPB3_HUMAN tRNA modification GTPase GTPBP3, mitochondrial [...] GTPBP3 , MTGP1Homo sapiens (Human) 492 AA O43819 SCO2_HUMAN Protein SCO2 homolog, mitochondrial SCO2 Homo sapiens (Human) 266 AA O95299 NDUAA_HUMAN NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 10, mitochondrial [...] NDUFA10 Homo sapiens (Human) 355 AA Q9Y3A0 COQ4_HUMAN Ubiquinone biosynthesis protein COQ4 homolog, mitochondrial [...] COQ4 , CGI-92Homo sapiens (Human) 265 AA P39210 MPV17_HUMAN Protein Mpv17 MPV17 Homo sapiens (Human) 176 AA Q9Y3D9 RT23_HUMAN Small ribosomal subunit protein mS23 [...] MRPS23 , CGI-138, HSPC329Homo sapiens (Human) 190 AA P41499 PTN11_RAT Tyrosine-protein phosphatase non-receptor type 11 [...] Ptpn11 Rattus norvegicus (Rat) 593 AA Q969S9 RRF2M_HUMAN Ribosome-releasing factor 2, mitochondrial [...] GFM2 , EFG2, MSTP027Homo sapiens (Human) 779 AA Q5JPH6 SYEM_HUMAN Nondiscriminating glutamyl-tRNA synthetase EARS2, mitochondrial [...] EARS2 , KIAA1970Homo sapiens (Human) 523 AA Q53S33 BOLA3_HUMAN BolA-like protein 3 BOLA3 Homo sapiens (Human) 107 AA Q12887 COX10_HUMAN Protoheme IX farnesyltransferase, mitochondrial [...] COX10 Homo sapiens (Human) 443 AA Q70HW3 SAMC_HUMAN Mitochondrial S-adenosylmethionine carrier protein [...] SLC25A26 , SAMCHomo sapiens (Human) 274 AA Q96BR5 COA7_HUMAN Cytochrome c oxidase assembly factor 7 [...] COA7 , C1orf163, RESA1, SELRC1Homo sapiens (Human) 231 AA P49916 DNLI3_HUMAN DNA ligase 3 [...] LIG3 Homo sapiens (Human) 1,009 AA Q13472 TOP3A_HUMAN DNA topoisomerase 3-alpha [...] TOP3A , TOP3Homo sapiens (Human) 1,001 AA P51570 GALK1_HUMAN Galactokinase [...] GALK1 , GALKHomo sapiens (Human) 392 AA Q9BZK7 TBL1R_HUMAN F-box-like/WD repeat-containing protein TBL1XR1 [...] TBL1XR1 , IRA1, TBLR1Homo sapiens (Human) 514 AA Q9H845 ACAD9_HUMAN Complex I assembly factor ACAD9, mitochondrial [...] ACAD9 Homo sapiens (Human) 621 AA Q07021 C1QBP_HUMAN Complement component 1 Q subcomponent-binding protein, mitochondrial [...] C1QBP , GC1QBP, HABP1, SF2P32Homo sapiens (Human) 282 AA Q330K2 NDUF6_HUMAN NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 [...] NDUFAF6 , C8orf38Homo sapiens (Human) 333 AA