P00367 DHE3_HUMAN Glutamate dehydrogenase 1, mitochondrial [...] GLUD1 , GLUDHomo sapiens (Human) 558 AA P08559 ODPA_HUMAN Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial [...] PDHA1 , PHE1AHomo sapiens (Human) 390 AA P13196 HEM1_HUMAN 5-aminolevulinate synthase, non-specific, mitochondrial [...] ALAS1 , ALAS3, ALASH, OK/SW-cl.121Homo sapiens (Human) 640 AA P18859 ATP5J_HUMAN ATP synthase-coupling factor 6, mitochondrial [...] ATP5PF , ATP5A, ATP5J, ATPMHomo sapiens (Human) 108 AA P22830 HEMH_HUMAN Ferrochelatase, mitochondrial [...] FECH Homo sapiens (Human) 423 AA P25705 ATPA_HUMAN ATP synthase subunit alpha, mitochondrial [...] ATP5F1A , ATP5A, ATP5A1, ATP5AL2, ATPMHomo sapiens (Human) 553 AA P28331 NDUS1_HUMAN NADH-ubiquinone oxidoreductase 75 kDa subunit, mitochondrial [...] NDUFS1 Homo sapiens (Human) 727 AA P40926 MDHM_HUMAN Malate dehydrogenase, mitochondrial [...] MDH2 Homo sapiens (Human) 338 AA P56181 NDUV3_HUMAN NADH dehydrogenase [ubiquinone] flavoprotein 3, mitochondrial [...] NDUFV3 Homo sapiens (Human) 108 AA Q00059 TFAM_HUMAN Transcription factor A, mitochondrial [...] TFAM , TCF6, TCF6L2Homo sapiens (Human) 246 AA Q13011 ECH1_HUMAN Delta(3,5)-Delta(2,4)-dienoyl-CoA isomerase, mitochondrial [...] ECH1 Homo sapiens (Human) 328 AA Q99798 ACON_HUMAN Aconitate hydratase, mitochondrial [...] ACO2 Homo sapiens (Human) 780 AA O43678 NDUA2_HUMAN NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 2 [...] NDUFA2 Homo sapiens (Human) 99 AA O75489 NDUS3_HUMAN NADH dehydrogenase [ubiquinone] iron-sulfur protein 3, mitochondrial [...] NDUFS3 Homo sapiens (Human) 264 AA P06576 ATPB_HUMAN ATP synthase subunit beta, mitochondrial [...] ATP5F1B , ATP5B, ATPMB, ATPSBHomo sapiens (Human) 529 AA P10809 CH60_HUMAN 60 kDa heat shock protein, mitochondrial [...] HSPD1 , HSP60Homo sapiens (Human) 573 AA P23368 MAOM_HUMAN NAD-dependent malic enzyme, mitochondrial [...] ME2 Homo sapiens (Human) 584 AA P30837 AL1B1_HUMAN Aldehyde dehydrogenase X, mitochondrial [...] ALDH1B1 , ALDH5, ALDHXHomo sapiens (Human) 517 AA P36542 ATPG_HUMAN ATP synthase subunit gamma, mitochondrial [...] ATP5F1C , ATP5C, ATP5C1, ATP5CL1Homo sapiens (Human) 298 AA P52815 RM12_HUMAN Large ribosomal subunit protein bL12m [...] MRPL12 , MRPL7, RPML12Homo sapiens (Human) 198 AA P54886 P5CS_HUMAN Delta-1-pyrroline-5-carboxylate synthase [...] ALDH18A1 , GSAS, P5CS, PYCSHomo sapiens (Human) 795 AA P78540 ARGI2_HUMAN Arginase-2, mitochondrial [...] ARG2 Homo sapiens (Human) 354 AA Q02218 ODO1_HUMAN 2-oxoglutarate dehydrogenase complex component E1 [...] OGDH Homo sapiens (Human) 1,023 AA Q96I99 SUCB2_HUMAN Succinate--CoA ligase [GDP-forming] subunit beta, mitochondrial [...] SUCLG2 Homo sapiens (Human) 432 AA O75947 ATP5H_HUMAN ATP synthase subunit d, mitochondrial [...] ATP5PD , ATP5H, My032Homo sapiens (Human) 161 AA