Q15118 PDK1_HUMAN [Pyruvate dehydrogenase (acetyl-transferring)] kinase isozyme 1, mitochondrial [...] PDK1 , PDHK1Homo sapiens (Human) 436 AA Q4G0N4 NAKD2_HUMAN NAD kinase 2, mitochondrial [...] NADK2 , C5orf33, MNADK, NADKD1Homo sapiens (Human) 442 AA Q96RR1 PEO1_HUMAN Twinkle mtDNA helicase [...] TWNK , C10orf2, PEO1Homo sapiens (Human) 684 AA Q9UKU7 ACAD8_HUMAN Isobutyryl-CoA dehydrogenase, mitochondrial [...] ACAD8 , ARC42, IBDHomo sapiens (Human) 415 AA P10809 CH60_HUMAN 60 kDa heat shock protein, mitochondrial [...] HSPD1 , HSP60Homo sapiens (Human) 573 AA P23368 MAOM_HUMAN NAD-dependent malic enzyme, mitochondrial [...] ME2 Homo sapiens (Human) 584 AA P36542 ATPG_HUMAN ATP synthase subunit gamma, mitochondrial [...] ATP5F1C , ATP5C, ATP5C1, ATP5CL1Homo sapiens (Human) 298 AA Q02218 ODO1_HUMAN 2-oxoglutarate dehydrogenase complex component E1 [...] OGDH Homo sapiens (Human) 1,023 AA P36776 LONM_HUMAN Lon protease homolog, mitochondrial [...] LONP1 , PRSS15Homo sapiens (Human) 959 AA P42126 ECI1_HUMAN Enoyl-CoA delta isomerase 1, mitochondrial [...] ECI1 , DCIHomo sapiens (Human) 302 AA P55809 SCOT1_HUMAN Succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial [...] OXCT1 , OXCT, SCOTHomo sapiens (Human) 520 AA Q16836 HCDH_HUMAN Hydroxyacyl-coenzyme A dehydrogenase, mitochondrial [...] HADH , HAD, HAD1, HADHSC, SCHADHomo sapiens (Human) 314 AA P00367 DHE3_HUMAN Glutamate dehydrogenase 1, mitochondrial [...] GLUD1 , GLUDHomo sapiens (Human) 558 AA P22830 HEMH_HUMAN Ferrochelatase, mitochondrial [...] FECH Homo sapiens (Human) 423 AA P25705 ATPA_HUMAN ATP synthase subunit alpha, mitochondrial [...] ATP5F1A , ATP5A, ATP5A1, ATP5AL2, ATPMHomo sapiens (Human) 553 AA P28331 NDUS1_HUMAN NADH-ubiquinone oxidoreductase 75 kDa subunit, mitochondrial [...] NDUFS1 Homo sapiens (Human) 727 AA P40926 MDHM_HUMAN Malate dehydrogenase, mitochondrial [...] MDH2 Homo sapiens (Human) 338 AA Q00059 TFAM_HUMAN Transcription factor A, mitochondrial [...] TFAM , TCF6, TCF6L2Homo sapiens (Human) 246 AA P05091 ALDH2_HUMAN Aldehyde dehydrogenase, mitochondrial [...] ALDH2 , ALDMHomo sapiens (Human) 517 AA P05166 PCCB_HUMAN Propionyl-CoA carboxylase beta chain, mitochondrial [...] PCCB Homo sapiens (Human) 539 AA P07954 FUMH_HUMAN Fumarate hydratase, mitochondrial [...] FH Homo sapiens (Human) 510 AA P11177 ODPB_HUMAN Pyruvate dehydrogenase E1 component subunit beta, mitochondrial [...] PDHB , PHE1BHomo sapiens (Human) 359 AA P17612 KAPCA_HUMAN cAMP-dependent protein kinase catalytic subunit alpha [...] PRKACA , PKACAHomo sapiens (Human) 351 AA P24752 THIL_HUMAN Acetyl-CoA acetyltransferase, mitochondrial [...] ACAT1 , ACAT, MATHomo sapiens (Human) 427 AA P45954 ACDSB_HUMAN Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial [...] ACADSB Homo sapiens (Human) 432 AA