A0A2H4FX70 · A0A2H4FX70_HUMAN
- ProteinGlutaryl-CoA dehydrogenase, mitochondrial
- GeneGCDH
- StatusUniProtKB unreviewed (TrEMBL)
- Organism
- Amino acids438 (go to sequence)
- Protein existenceEvidence at transcript level
- Annotation score2/5
Function
Catalytic activity
- glutaryl-CoA + oxidized [electron-transfer flavoprotein] + 2 H+ = (2E)-butenoyl-CoA + reduced [electron-transfer flavoprotein] + CO2
Cofactor
Pathway
Amino-acid metabolism; lysine degradation.
Amino-acid metabolism; tryptophan metabolism.
GO annotations
Aspect | Term | |
---|---|---|
Cellular Component | mitochondrion | |
Molecular Function | acyl-CoA dehydrogenase activity | |
Molecular Function | flavin adenine dinucleotide binding |
Keywords
- Molecular function
- Ligand
Enzyme and pathway databases
Names & Taxonomy
Protein names
- Recommended nameGlutaryl-CoA dehydrogenase, mitochondrial
- EC number
Gene names
Organism names
- Organism
- Taxonomic lineageEukaryota > Metazoa > Chordata > Craniata > Vertebrata > Euteleostomi > Mammalia > Eutheria > Euarchontoglires > Primates > Haplorrhini > Catarrhini > Hominidae > Homo
Accessions
- Primary accessionA0A2H4FX70
Subcellular Location
PTM/Processing
Structure
Family & Domains
Features
Showing features for domain.
Type | ID | Position(s) | Description | |||
---|---|---|---|---|---|---|
Domain | 62-172 | Acyl-CoA dehydrogenase/oxidase N-terminal | ||||
Sequence: TDEILIRDTFRTYCQERLMPRILLANRNEVFHREIISEMGELGVLGPTIKGYGCAGVSSVAYGLLARELERVDSGYRSAMSVQSSLVMHPIYAYGSEEQRQKYLPQLAKGE | ||||||
Domain | 176-269 | Acyl-CoA oxidase/dehydrogenase middle | ||||
Sequence: CFGLTEPNSGSDPSSMETRAHYNSSNKSYTLNGTKTWITNSPMADLFVVWARCEDGCIRGFLLEKGMRGLSAPRIQGKFSLRASATGMIIMDGV | ||||||
Domain | 289-428 | Acyl-CoA dehydrogenase/oxidase C-terminal | ||||
Sequence: CLNNARYGIAWGVLGASEFCLHTARQYALDRMQFGVPLARNQLIQKKLADMLTEITLGLHACLQLGRLKDQDKAAPEMVSLLKRNNCGKALDIARQARDMLGGNGISDEYHVIRHAMNLEAVNTYEGTHDIHALILGRAM |
Sequence similarities
Belongs to the acyl-CoA dehydrogenase family.
Keywords
- Domain
Family and domain databases
Sequence
- Sequence statusComplete
- Length438
- Mass (Da)48,145
- Last updated2018-02-28 v1
- Checksum415B88450027BB63